This article reports a case of perinatal mesenchymal hepatic hamartoma and reviews the literature on the subject. A fetus presented with polyhydramnios and a large multiloculated cystic abdominal mass at 33 weeks of gestation. The ultrasound appearance was most consistent with a mesenteric cyst. Prenatal drainage was considered, due to the size of the lesion. However, a conservative management was opted for. A female infant was born at 35 weeks by classical cesarean section. The immediate postnatal period was characterized by hemodynamic instability. Laparotomy revealed a pedunculated mesenchymal hamartoma of the liver, which could not completely be resected. The infant had an uneventful postoperative recovery and is doing well at 6 months of age. Hepatic mesenchymal hamartoma are rare benign tumors. Most cases are detected in early childhood. They usually present as a cystic rapidly growing abdominal mass. Prenatal diagnosis remains challenging. In children diagnosed in the perinatal period, the outcome seems worse and determined by the compressive effect of the mass. Copyright

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Keywords Abdominal cyst, Fetal therapy, Mesenchymal hamartoma, Perinatal mortality, Prenatal diagnosis
Persistent URL dx.doi.org/10.1159/000212057, hdl.handle.net/1765/24920
Citation
Cornette, J., Festen, S., van den Hoonaard, T.L., & Steegers-Theunissen, R.P.M.. (2009). Mesenchymal hamartoma of the liver: A benign tumor with deceptive prognosis in the perinatal period: Case report and review of the literature. Fetal Diagnosis and Therapy, 25(2), 196–202. doi:10.1159/000212057