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patient spg 7 mutation brain death brain organ death mutation spg 4 region bulbar donor symptom onset brainstem re flexes study organ donors bulbar region symptoms involvement disease spastic criteria sclerosis donation neurol van den berg brainstem spastic paraplegia finition phenotype score scale spastic paraparesis right bulbar region involvement organ donor syndrome symptom onset neurology autosomal paraplegia organ donation pls phenotype family diagnosis analysis dorsal column impairment motor cause glasgow coma scale response neuron netherland 14 patients bulbar region university arch neurol paraparesi erasmus mc j hum genet transplant brain damage re flexes brugman www.archneurol.com center adult-onset transplantation procurement wokke disease onset leg involvement wijdick characteristic recognition feature adult-onset umn syndrome spg 7 mutations amyotrophic reason urgency
2 Most Recent Publications
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Imminent brain death: Point of departure for potential heart-beating organ donor recognition
(Article)
Groot, Y.J. de Jansen, N.E. Kompanje, E.J.O. Bakker, J. Kuiper, M.A. Aerdts, S. Maas, A.I.R. Wijdicks, E.F.M. Leiden, H.A. van Hoitsma, A.J. Kremer, B.H.P. |
2010-09-01
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Differentiation of hereditary spastic paraparesis from primary lateral sclerosis in sporadic adult-onset upper motor neuron syndromes
(Article)
Brugman, F. Veldink, J.H. Bruyn, R.P.M. Kuks, J.B.M. Robberecht, W. Wokke, J.H.J. Berg, L.H. van den Franssen, H. Visser, M. de Vianney de Jong, J.M.B. Faber, C.G. Kremer, B.H.P. Schelhaaspieter, J. Doorn, V. Verschuuren, J.J. |
2009-04-01
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