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/ercc sequence repair xpbc /ercc gene region promoter xpbc /ercc promoter protein fragment analysis transcription probe group element excision plasmid complementation ercc -3 cdna position nucleotide expression binding figure cap site helicase defect genomic xpllbe clone mutation ercc -3 oligonucleotide ercc -3 gene activity blot analysis acids research domain transfection hela tk result xpbc /ercc xp complementation groups nature factor patient experiment level fibroblast splice disorder transcription initiation site xpbc /ercc cdna mutant transcript filter rodent yeast hoeijmaker 4 bp insertion function initiation xpbciercc number hela cells cat activity research acid sequence assay deletion extension primer motif wild-type xeroderma nucleotide sequence signal hybridized restriction van der eb cre /tre element