Bronsveld, I.

chloride patient fibrosis response conductance disease mutation secretion channel tissue sweat transport figure sibling chloride secretion difference cf patients phenotype measurement function study carbachol individual histamine chapter epithelium number pancreatic presence transmembrane protein chloride conductance expression secretory cftr gene genotype solution dizygou monozygou regulator value result 2 +- delta cf disease membrane airway epithelial factor fevperc control basal j clin fi brosis analysis bijman j table intrapair boucher rc addition group genet jonge hr disease severity brosi chloride channels apical tract biopsy influence isoprenaline defect cohort apical membrane germany bijman severity hospital sequence sweat test