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scopus: 7005850133

Bootsma, D.

(Dirk Bootsma)

Supervisor (promotor) of 36 dissertations


repair protein sequence mouse figure analysis region cancer mutation wild-type group defect probe yeast transcription fragment clone expression damage lesion patient level syndrome excision xpc-hr 23b result recombination fibroblast genomic hoeijmaker function xeroderma ercc 1 blot analysis nucleotide allele pigmentosum ttd mice tumor research promoter genome domain acids research complementation experiment dna repair bootsma number mutant mrad 54 / transcript dna damage xeroderma pigmentosum synthesis strand xpc-hr homolog position ercc 1 protein helicase /ercc csb / mice sensitivity survival ercc -7 effect binding activity enzyme homology uv-induced csb / acid sequence 1*292 cockayne factor hhr 23 proteins erccg antibody




10 Most Recent Publications

UVB radiation-induced cancer predisposition in Cockayne syndrome group A (Csa) mutant mice. (Article)
Meira, L. Gorgels, T.G.M.F. Friedberg, E.C. Horst, G.T.J. van der Wit, J. de Velasco-Miguel, S. Richardson, J.A. Kamp, Y. Vreeswijk, M.P. Smit, B. Bootsma, D. Hoeijmakers, J.H.J.
2002-05-16
MammalianCry1 and Cry2 are essential for maintenance of circadian rhythms (Letter To Editor)
Horst, G.T.J. van der Muijtjens, M. Buijs, R. Bootsma, D. Hoeijmakers, J.H.J. Yasui, A. Kobayashi, K. Takano, R. Kanno, S-I. Takao, M. Wit, J. de Verkerk, A. Eker, A.P.M. Leenen, D. van
1999-04-15
Mouse model for the DNA repair/basal transcription disorder Trichothiodystrophy reveals cancer predisposition. (Article)
Boer, J. de Steeg, H. van Bootsma, D. Hoeijmakers, J.H.J. Weeda, G. Berg, R.J.W. Garssen, J. Wit, J. de Oostrom, C.T.M. van Beems, R.B. Horst, G.T.J. van der Kreijl, C.F. van Gruijl, F.R. de
1999-01-01
Mouse model for the DNA repair/basal transcription disorder trichothiodystrophy reveals cancer predisposition (Article)
Boer, J. de Kreijl, C.F. van Beems, R.B. Hoeijmakers, J.H.J. Horst, G.T.J. van der Weeda, G. Gruijl, F.R. de Bootsma, D. Steeg, H. van Berg, R.J.W. Garssen, J. Wit, J. de Oostrum, C.T. van
1999-01-01
Xeroderma pigmentosum group C complex is the initiator of global genome repair. (Miscellaneous)
Sugasawa, K. Ng, J.M.Y. Masutani, C. Spek, P.J. van der Eker, A.P.M. Hanaoka, F. Bootsma, D. Hoeijmakers, J.H.J.
1998-08-01
Defective transcription-coupled repair in Cockayne syndrome B mice is associated with skin cancer predisposition. (Article)
Horst, G.T.J. van der Steeg, H. van Bootsma, D. Hoeijmakers, J.H.J. Berg, R.J.W. Gool, A.J. van Wit, J. de Weeda, G. Morreau, H. Beems, R.B. Kreijl, C.F. van Gruijl, F.R. de
1997-05-02
Disruption of mouse ERCC1 results in a novel repair syndrome with growth failure, nuclear abnormalities and senescence. (Article)
Weeda, G. Donker, I. Wit, J. de Morreau, H. Janssens, R. Vissers, C.J. Nigg, A. Steeg, H. van Bootsma, D. Hoeijmakers, J.H.J.
1997-01-01
Disruption of mouse RAD54 reduces ionizing radiation resistance and homologous recombination. (Article)
Essers, J. Hendriks, R.W. Swagemakers, S.M.A. Troelstra, C. Wit, J. de Bootsma, D. Hoeijmakers, J.H.J. Kanaar, R.
1997-01-01
The Cockayne syndrome B protein, involved in transcription-coupled repair resides in a RNA polymerase II-containing complex. (Article)
Gool, A.J. van Citterio, E. Rademakers, S. Os, R. van Vermeulen, W. Constantinou, A. Egly, J-M. Bootsma, D. Hoeijmakers, J.H.J.
1997-01-01
Mammalian nucleotide excision repair and syndromes. (Article)
Vermeulen, W. Boer, J. de Weeda, G. Winkler, G.S. Bootsma, D. Egly, J-M. Hoeijmakers, J.H.J. Citterio, E. Gool, A.J. van Horst, G.T.J. van der Jaspers, N.G.J. Laat, W.L. de Sijbers, A.M. Spek, P.J. van der Sugasawa, K.
1997-01-01