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Bijvoet, A.G.
( A.G. Bijvoet)
glucosidase enzyme muscle mouse disease glycogen tissue activity lysosomal gsdii knockout storage heart glucosidase activity expression enzyme replacement therapy knockout mice model production gland protein genetic reuser figure rabbit precursor patient therapy cho cells transgene deficiency rhgaa replacement a.j.j table placental acid animal fraction antibody wild-type study analysis glucosidase gene fragment liver fibroblast level lysosomal glycogen storage injection ko mice 76 kda sequence 1-casein result gsdii knockout mice 110 kda precursor 6 weeks medium knockout mouse glycogen storage section lysosomal storage diseases sample microscopy electron treatment acids research ploeg natl acad glucosidase antibodies enzyme activity electron microscopy glycogenosis type ii cho cell medium knockout mouse model uptake c 57bl mice rabbit antibodies 13 weeks mouse milk
4 Most Recent Publications
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Therapy for Glycogen Storage Disease Type II: Acid a-glucosidase production in milk and enzyme replacement therapy in a mouse model
(Doctoral Thesis)
Bijvoet, A.G. |
1999-06-16
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Human acid alpha-glucosidase from rabbit milk has therapeutic effect in mice with glycogen storage disease type II
(Article)
Bijvoet, A.G. Reuser, A.J.J. Ploeg, A.T. van der Hirtum, H. van Kroos, M.A. Kamp, E.H. van de Schoneveld, O. Visser, P. Brakenhoff, J.P. Weggeman, M. Corven, E.J. van |
1999-01-01
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Generalized glycogen storage and cardiomegaly in a knockout mouse model of Pompe disease
(Article)
Bijvoet, A.G. Ploeg, A.T. van der Reuser, A.J.J. Kamp, E.H. van de Kroos, M.A. Ding, J-H. Yang, B.Z. Visser, P. Bakker, C.E. Verbeet, M.P. Oostra, B.A. |
1998-01-01
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Recombinant human acid alpha-glucosidase: high level production in mouse milk, biochemical characteristics, correction of enzyme deficiency in GSDII KO mice
(Article)
Bijvoet, A.G. Kroos, M.A. Pieper, F.R. Vliet, M. van der Boer, H.A. Ploeg, A.T. van der Verbeet, M.P. Reuser, A.J.J. |
1998-01-01
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