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Yang, B.Z.

(Bing Yang)


glucosidase knockout muscle knockout mice disease glycogen mouse tissue model gsdii storage activity heart lysosomal wild-type 6 weeks knockout mouse glucosidase activity 13 weeks genetic animal cassette analysis figure mouse model gaa gene lysosomal glycogen storage acid maltase deficiency glycogenosi quail deficiency fibre muscle fibres acid phosphatase animal models electron femoral muscle primer gsdii knockout mice glycogen storage disease reuser sequence knockout mouse model birth combination murine gaa gene murine acids research clone pompe femoral glucosidase gene japanese quail placental acid study electron microscopy patient fragment enzyme glucosidase deficiency pathology protein symptom liver genomic cattle japanese microscopy a.j.j staining lysosome maltase recombination round heart disease heart muscle development glycogenosis type ii vacuole species sense




1 Most Recent Publications

Generalized glycogen storage and cardiomegaly in a knockout mouse model of Pompe disease (Article)
Bijvoet, A.G. Ploeg, A.T. van der Reuser, A.J.J. Kamp, E.H. van de Kroos, M.A. Ding, J-H. Yang, B.Z. Visser, P. Bakker, C.E. Verbeet, M.P. Oostra, B.A.
1998-01-01