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hearing infant hearing loss response i –v interval children auditory interval patient result sensorineural hearing loss hearing screening screening threshold study measurement postconceptional level brainstem fi tting model postconceptional age abr measurement population disease sensorineural latencie risk factors development preterm conductive hearing loss factor maturation birth conductive model analysis language development tting preterm infants range nicu infants table i –iii system language control hospital abr results 0.23 value bow tie pattern effect 1.60 contralateral function pompe disease fi rst auditory brainstem responses i –v intervals vancomycin pompe follow-up netherland peak i sepsis intelligence peak iii auditory system treatment neuropathy peaks iii score sophia abr threshold meningiti prevalence pattern coenraad 90 db nhl enzyme replacement therapy