Myotonic dystrophia type I or Steinert's disease is a progressive multisystemic-inherited neuromuscular disease. Higher sensitivity to sedatives, anaesthetic, and neuromuscular blocking agents may result in cardiovascular and respiratory complications. We describe the anaesthesiological and ventilatory measures in a 43-year-old patient with Steinert's disease successfully undergoing cardiac surgery.

doi.org/10.1111/j.1540-8191.2007.00349.x, hdl.handle.net/1765/36337
Journal of Cardiac Surgery
Erasmus MC: University Medical Center Rotterdam

Klompe, L., Lancé, M., van der Woerd, D., Scohy, T., & Bogers, A. (2007). Anaesthesiological and ventilatory precautions during cardiac surgery in Steinert's disease: A case report. Journal of Cardiac Surgery, 22(1), 74–75. doi:10.1111/j.1540-8191.2007.00349.x