Congenital mesoblastic nephroma (CMN) is a rare pediatric renal tumor with low malignant potential that most commonly occurs early in infancy. Treatment strategies are based on the few published CMN series, while a significant number of CMN patients have been described in case reports. The aim of this narrative review was to create an up-to-date overview of the literature. Complete surgical removal is curative in most cases. The risk of treatment-related mortality (both surgery- and chemotherapy-related) is relatively high in the first weeks of life, indicating that these young patients deserve special attention with respect to timing and type of treatment.

, , , , , , , ,,
Pediatric Blood & Cancer
Department of Pediatrics

Gooskens, S., Houwing, M. E., Vujanic, G., Dome, J., Diertens, T., Coulomb-L'Herminé, A., … van den Heuvel-Eibrink, M. (2017). Congenital mesoblastic nephroma 50 years after its recognition: A narrative review. Pediatric Blood & Cancer (Vol. 64). doi:10.1002/pbc.26437