Clinical features and treatment of keratoderma hereditaria mutilans (Vohwinkel's syndrome) are described in an 11-year-boy. The disease, in particular the mutilating complications (pseudo-ainhum), responded satisfactorily to the oral administration of etretinate, an aromatic retinoid.

doi.org/10.1001/archderm.117.4.225, hdl.handle.net/1765/107185
Archives of Dermatology

Chang Sing Pang, A.F.I. (Albert F. I.), Oranje, A. P., Vuzevki, V.D. (Vojislav D.), & Stolz, E. (1981). Successful Treatment of Keratoderma Hereditaria Mutilans With an Aromatic Retinoid. Archives of Dermatology, 117(4), 225–228. doi:10.1001/archderm.117.4.225