<p>Cystic Fibrosis (CF) is a life-long genetic disease, causing increased energy needs and a healthy diet with a specific nutrient distribution. Nutritional status is an indicator of disease prognosis and survival. This study aimed at assessing the effectiveness of a self-management mobile app in supporting patients with CF to achieve the dietary goals set by the CF nutrition guidelines. A clinical trial was conducted in pancreatic insufficient children with CF, followed in six European CF centres, where the self-management app developed within the MyCyFAPP project was used for six months. To assess secondary outcomes, three-day food records were compiled in the app at baseline and after 3 and 6 months of use. Eighty-four subjects (mean 7.8 years old) were enrolled. Compared to baseline, macronutrient distribution better approximated the guidelines, with protein and lipid increasing by 1.0 and 2.1% of the total energy intake, respectively, by the end of the study. Consequently, carbohydrate intake of the total energy intake decreased significantly (−2.9%), along with simple carbohydrate intake (−2.4%). Regarding food groups, a decrease in ultra-processed foods was documented, with a concomitant increase in meat and dairy. The use of a self-management mobile app to self-monitor dietary intake could become a useful tool to achieve adherence to guideline recommendations, if validated during a longer period of time or against a control group.</p>

doi.org/10.3390/nu13061801, hdl.handle.net/1765/136678
Erasmus MC: University Medical Center Rotterdam

Joaquim Calvo-Lerma, Mieke Boon, J Hulst, Carla Colombo, Inês Asseiceira, Maria Garriga, … Carmen Ribes-Koninckx. (2021). Change in nutrient and dietary intake in european children with cystic fibrosis after a 6-month intervention with a self-management mhealth tool. Nutrients, 13(6). doi:10.3390/nu13061801