A chordoma which occurs as a primary tumour outside the axial skeleton is known as an extra-axial chordoma, parachordoma or chordoma periphericum. It is extremely rare and therefore survival, recurrence and the rates of metastasis are not known. Whilst few recurrences have been described, the extra-axial chordoma has the potential for late recurrence at up to 12 years. Metastases are even less frequent. We report the case of a 56-year-old woman who developed an extra-axial chordoma of the right thoracic wall in close relationship with the tenth rib. The tumour was completely removed and the prognosis is excellent.

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doi.org/10.1302/0301-620X.88B9.17873, hdl.handle.net/1765/14897
Journal of Bone and Joint Surgery: British Volume
Erasmus MC: University Medical Center Rotterdam

van Akkooi, A.C.J, van Geel, A.N, Bessems, J.H.J.M, & den Bakker, M.A. (2006). Extra-axial chordoma. Journal of Bone and Joint Surgery: British Volume, 88(9), 1232–1234. doi:10.1302/0301-620X.88B9.17873