A 10-year-old girl with Apert syndrome underwent a Le Fort III osteotomy with the positioning of internal and external distraction devices. The operation was straightforward with no intraoperative complications. Very soon after completion of surgery an anisocoria (unilateral dilation of a pupil) was noticed. This was followed by intracranial oedema which was fatal. The aetiology was dissection of the right internal carotid artery is reported. The complications of Le Fort osteotomies are discussed regarding patients with complex syndromal craniosynostosis and midface hypoplasia, such as Apert syndrome.

Additional Metadata
Keywords Apert, cerebral, complication, dissection, midface distraction
Persistent URL dx.doi.org/10.1016/j.jcms.2010.02.002, hdl.handle.net/1765/28278
Journal Journal of Cranio-Maxillofacial Surgery
Citation
Nout, E, Mathijssen, I.M.J, van der Meulen, J.J.N.M, van Veelen-Vincent, M.L.C, Koning, A.H.J, Leguin, M, & Wolvius, E.B. (2010). Internal carotid dissection after Le Fort III distraction in Apert syndrome: A case report. Journal of Cranio-Maxillofacial Surgery, 38(7), 529–533. doi:10.1016/j.jcms.2010.02.002