Objective: We studied the long-term results of vertical plication repair of Ebstein's anomaly according to Carpentier. Methods: Between 1988 and 2007, 28 patients (mean age 28.8 ± 15.7 years, range 4-58 years) underwent vertical plication repair of Ebstein's anomaly. At operation the anomaly was classified according to Carpentier. In three patients (11%) a cavopulmonary shunt was added at the repair on the indication of impaired right ventricular function. Results: There was no operative mortality. Early mortality was 3.6% (one patient). Actuarial survival and actuarial freedom from reoperation at 19 years were 96% (95% CI; 96-97%) and 72% (95% CI; 53-92%), respectively. Six patients required reoperation, with a successful re-repair in three patients. Mean duration of follow-up was 10.7 ± 6.5 years. One year postoperatively, tricuspid incompetence had decreased significantly (p < 0.001), as had New York Heart Association (NYHA) functional class (p < 0.001). In addition, exercise tolerance had increased (70 ± 19% to 92 ± 9% of predicted values, p < 0.05). Both tricuspid function and NYHA functional class remained essentially unchanged at the end of follow-up, indicating durable haemodynamic and functional results. Conclusion: This study demonstrates favourable long-term results following vertical plication repair of Ebstein's anomaly with low mortality, acceptable morbidity and good haemodynamic and functional results.

Additional Metadata
Keywords Acyanotic, Cardiac congenital, Cyanotic, Tricuspid valve
Persistent URL dx.doi.org/10.1016/j.ejcts.2008.03.048, hdl.handle.net/1765/30210
Journal European Journal of Cardio-Thoracic Surgery
Note Free full text at PubMed
Palmen, M, de Jong, P.L, Klieverik, L.M.A, Venema, A.C, Meijboom, F.J, & Bogers, A.J.J.C. (2008). Long-term follow-up after repair of Ebstein's anomaly. European Journal of Cardio-Thoracic Surgery, 34(1), 48–54. doi:10.1016/j.ejcts.2008.03.048