Osteopathia striata with cranial sclerosis (OS-CS) is a rare skeletal dysplasia characterized by linear striations of the long bones, osteosclerosis of the cranium, and extraskeletal anomalies. Osteosclerosis of the cranial and facial bones can lead to disfigurement and to disability due to the pressure on the cranial nerves. We report two cases of OS-CS where surgically assisted rapid maxillary expansion was performed for widening the extremely narrow maxilla. One should be aware of the disease-related problems and the possible complications that might occur with this type of patient.

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doi.org/10.1597/07-016, hdl.handle.net/1765/32415
Cleft Palate - Craniofacial Journal
Erasmus MC: University Medical Center Rotterdam

Koudstaal, M., Wolvius, E., Ongkosuwito, E., & van der Wal, K. (2008). Surgically assisted rapid maxillary expansion in two cases of osteopathia striata with cranial sclerosis. Cleft Palate - Craniofacial Journal, 45(3), 337–342. doi:10.1597/07-016