A variant form of Creutzfeldt-Jakob disease (vCJD) has had major impact in Europe during the last decade. In this article, we review the aetiology of vCJD and its relation with bovine spongiform encephalopathy. Further, treatment of the disease, the strategies focusing on prevention of transmission, future prospects, and the limitations encountered in epidemiological research of vCJD are discussed.

CJD surveillance in the Netherlands is carried out as part of the EU Concerted Action on the Epidemiology of CJD and the EU Concerted Action on Neuropathology of CJD, both funded through the BIOMED II programme, and is supported by the Dutch Ministry of Health.
doi.org/10.1023/A:1024683119263, hdl.handle.net/1765/57985
European Journal of Epidemiology
Erasmus MC: University Medical Center Rotterdam

Croes, E., & van Duijn, C. (2003). Variant Creutzfeldt-Jakob disease. European Journal of Epidemiology (Vol. 18, pp. 473–477). doi:10.1023/A:1024683119263