Kennedy disease is caused by an enlarged trinucleotide repeat sequence within the androgen receptor gene. We report here seven male patients with a benign motor neuron syndrome highly analogous to Kennedy disease but with a normal trinucleotide repeat.

Androgen receptor gene, Androgen sensitivity, Kennedy disease, Motor neuron disease, Trinucleotide repeat
dx.doi.org/10.1016/0022-510X(95)00064-9, hdl.handle.net/1765/66035
Journal of the Neurological Sciences
Department of Neurology

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