The authors describe a case of split notochord syndrome with a neuroenteric fistula in a newborn presenting with meningitis. Associated anomalies included agenesis of the corpus callosum, short colon, malrotation, epispadias, and an abnormally high bifurcation of the abdominal aorta and inferior vena cava. The embryological mechanisms and etiologic theories are discussed in short.

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doi.org/10.1016/j.jpedsurg.2006.09.070, hdl.handle.net/1765/73174
Journal of Pediatric Surgery
Department of Surgery

van Ramshorst, G., Lequin, M., Mancini, G., & van de Ven, C. (2006). A case of split notochord syndrome: a child with a neuroenteric fistula presenting with meningitis. Journal of Pediatric Surgery, 41(12). doi:10.1016/j.jpedsurg.2006.09.070