Superior semicircular canal dehiscence syndrome: Diagnosis and transmastoid surgical treatment

We describe two patients with superior semicircular canal dehiscence syndrome (SSCD) as the etiologic factor for hearing impairment. SSCD should be considered in the case of an unexplained hearing loss to prevent a futile middle ear exploration with ossiculoplasty and/or stapedotomy because otosclerosis is suspected. Differentiation between SSCD and otosclerosis using additional examinations is easy and should be performed. The transmastoid approach provides a good alternative to the better known middle fossa approach when treatment is needed.