Partial anomalous pulmonary venous connection (PAPVC) is defined to exist when some but not all venous drainage enters the left atrium, while the remaining veins connect to the right-sided circulation. Scimitar syndrome is a specialized example, in which an anomalous pulmonary vein descends from the right lung and drains into the inferior caval vein. PAPVC is associated with sinus venosus-type atrial septal defect (ASD). Diagnosis was, in the past, based on echocardiographic imaging and could be difficult. Multislice spiral computed tomography and magnetic resonance imaging improved the imaging quality. The surgical correction is dependent on the type of anomalous connection and the presence of an ASD. Outcome is good but obstructed venous return is an important issue.

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doi.org/10.1093/mmcts/mmt001, hdl.handle.net/1765/88353
Multimedia manual of cardiothoracic surgery : MMCTS / European Association for Cardio-Thoracic Surgery
Department of Cardio-Thoracic Surgery

van de Woestijne, P.C, Verberkmoes, N.J, & Bogers, A.J.J.C. (2013). Partial anomalous pulmonary venous connection (including scimitar syndrome). Multimedia manual of cardiothoracic surgery : MMCTS / European Association for Cardio-Thoracic Surgery, 2013. doi:10.1093/mmcts/mmt001